What is epidermolysis bullosa?

What is epidermolysis bullosa? What are its symptoms? How can it be treated? How can epidermolysis bullosa be relieved?

Epidermolysis bullosa is characterized by a problem of the junction between the epidermis and the dermis, which results in a bullous detachment and a skin abrasion. These bubbles generally appear after light injuries or frictions and can be localized anywhere on the body as well as on internal tissues.

The term of epidermolysis bullosa includes different skin pathologies, which are generally hereditary. Four big categories characterize this group, which includes epidermolysis bullosa simplex, dystrophic epidermolysis bullosa, junctional epidermolysis bullosa, and to a certain extent, Kindler’s syndrome. These forms differ by the localization of the rupture between the dermis and the epidermis.

Children suffering from epidermolysis bullosa are often called “butterfly children”, to reflect the fragility of their skin.

According to different epidemiological data, epidermolysis bullosa affects between 1 out of 20,000 and 1 out of 125,000 people. Dependant on the mutation type involved, transmission can be autosomal dominant or autosomal recessive.

What are the symptoms of epidermolysis bullosa?

In epidermolysis bullosa, symptoms and damages often accompany the formation of bubbles, like the deformation or loss of nails, hyperkeratosis, ocular damage,  sometimes major under-nutrition, chronic skin infections, retraction and synechia of the extremities, growth retardation, skin cancers.

How can epidermolysis bullosa be treated?

There are no existing treatments which can cure epidermolysis bullosa. The strategy is to avoid the formation of bubbles by carefully protecting the skin, avoiding impacts, preventing secondary infections and treating the wounds. These treatments are essentially done by using bandages that improve healing and minimize the risk of infection. Hydrating products are used daily to ensure a good skin quality and minimize the formation of bubbles.

Gene therapy studies are currently being led (Therapeuskin for example), but to date, no large-scale clinical trial results have been published yet.

How can epidermolysis bullosa be relieved?

 

The Hydrating Gel Plus HS developed by Skintifique has very strong hydrating and soothing properties. This product is used daily in addition to their treatment by some people suffering from epidermolysis bullosa. Some use it in a localized way, while others use it on their whole body. Of course, this gel does not cure epidermolysis bullosa, but the results generally are very good and provide a clear improvement of these people’s quality of life. See for instance Alexia’s interview.

Indeed, the Hydrating Gel Plus HS brings a real improvement of the skin’s quality, which becomes more supple and less dry. According to the experience of users suffering from epidermolysis bullosa, this gel can be used 2 to 3 times less than classic hydrating products that they were using before while getting an equivalent moisturising sensation and improving the quality of their skin.

These results are explained by the limited number of ingredients contained in the Hydrating Gel Plus HS, and the very innovative molecular structure of this gel-cream which ensures an exceptionally strong and deep hydration, and a long-lasting soothing effect.

If you are suffering from epidermolysis bullosa, and you would like to use our products, please contact us directly by clicking here to learn more about the use of our products, and the special conditions offered by Skintifique for people suffering from epidermolysis bullosa.

 

Do you suffer from epidermolysis bullosa?

Recommended skin care for epidermolysis bullosa

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An exceptionally pure head-to-toe hydrating cream. It provides an intense and long-lasting moisturising, soothes and helps repair skin. Suitable for babies, children & adults.

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A pack of 2 tubes of Hydrating Gel Plus HS (2x40ml) which offers significant cost savings for persons who need large volumes of this product. Moisturises, soothes and helps repair.

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A pack of 3 tubes of Hydrating Gel Plus HS (3x40ml) which offers significant cost savings for persons who need large volumes of this product. Moisturises, soothes and helps repair.

What are the results of Skintifique products on epidermolysis bullosa?

Alexia, 35 years old, is a young woman who suffers from epidermolysis bullosa. She usually uses a classic moisturiser, which she applies at least twice a day: after her shower and after care / bandages.

Alexia has started using the Hydrating Gel Plus HS and has quickly felt real benefits on the quality of her skin. After using it for one week, she has noticed that her skin is more elastic and less dry, indicating that these changes had also been noted by the nurses in charge of her cares and bandages. She also indicated that the gel really soothes the itching. 

In addition, Alexia had quickly decreased the quantity of Hydrating Gel Plus HS which she applies daily. Only one daily application is now needed, after her cares.

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